What is Nevus Spilus

Onset: They may appear at any age but usually develop before adulthood and follow a benign persistent course. Lesions can appear at birth or in early infancy as light colored café au lait macules. Pigmented macules and papules then develop over a period of months to years.
Cause: The anatomic position or time of onset is not related to sun exposure.
Origin: It has been suggested that nevus spilus is a subtype of congenital melanocytic nevus.
Size: Lesions may be very large. There is considerable variation in size, ranging from 1 to 20 cm.
Shape: Oval or irregularly shaped
Appearance: It is a common hairless, brown lesion that is dotted with darker brown-to-black spots. The brown area is usually flat, and the black dots may be slightly elevated and contain typical nevus cells.
Special features: The background hyperpigmentation histologically has the features of a lentigo or café au lait macule. The spots may be lentigines, junctional, compound, or intraepidermal nevi.
Treatment: Routine excision is not necessary. Biopsy suspicious areas. nevus spilus is flat and necessitates excision and closure if the patient desires removal.